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Eccrine angiomatous hamartoma
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Eccrine angiomatous hamartoma

Contributors: Nayan Lamba BA, Susan Burgin MD, Lowell A. Goldsmith MD, MPH
Other Resources UpToDate PubMed

Synopsis

Eccrine angiomatous hamartoma (EAH) is a rare benign tumor characterized by the proliferation of eccrine and vascular elements in the dermis.

EAH typically presents as a red, violaceous, or brownish nodule or plaque on an extremity. Papules or macules are less frequently seen. The face, neck, and trunk may also be primary sites of involvement. Patients report variable levels of pain. This is thought to occur as a result of small nerves that are seen on electron microscopy in close proximity to the eccrine and vascular structures. Hypertrichosis of the tumor is encountered in most cases. Hyperhidrosis is an additional diagnostic feature that is seen in under half of reported cases.

EAH is classically solitary; however, multiple tumors in a Blaschkoid or segmental distribution have been described. EAH grows proportionately with the affected individual.

Females and males are equally affected.

Codes

ICD10CM:
Q85.81 – PTEN hamartoma tumor syndrome

SNOMEDCT:
239115005 – Eccrine angiomatous hamartoma

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Last Updated:07/13/2016
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Eccrine angiomatous hamartoma
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A medical illustration showing key findings of Eccrine angiomatous hamartoma : Hypertrichosis, Smooth nodule, Smooth plaque, Hyperhidrosis
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