Congenital smooth muscle hamartomas develop during fetal life and are characterized by localized proliferations of smooth muscle bundles in the dermis with overlying vellus hairs. Congenital smooth muscle hamartomas may be noticed at birth or during early infancy. There are no systemic symptoms. The estimated prevalence is 1 in 2600 births with a slight male predominance.
Smooth muscle hamartomas are benign and, thus, the prognosis is excellent. Pigmentation and hair tend to become less noticeable with age.
Smooth muscle hamartoma in Infant/Neonate
Alerts and Notices
Important News & Links
Synopsis
Codes
ICD10CM:
Q85.9 – Phakomatosis, unspecified
SNOMEDCT:
239145008 – Diffuse smooth muscle hamartoma
Q85.9 – Phakomatosis, unspecified
SNOMEDCT:
239145008 – Diffuse smooth muscle hamartoma
Look For
Subscription Required
Diagnostic Pearls
Subscription Required
Differential Diagnosis & Pitfalls
To perform a comparison, select diagnoses from the classic differential
Subscription Required
Best Tests
Subscription Required
Management Pearls
Subscription Required
Therapy
Subscription Required
References
Subscription Required
Last Updated:10/01/2018
Smooth muscle hamartoma in Infant/Neonate
